Search Back New search Go to resultsDiseaseMain groupPediatric Oncology and HematologyProtocol groupHematologic Diseases (ped.)DiseaseHemophagocytic LymphohistiocytosisSubgroupICD10D76.1MeSHLymphohistiocytosis, HemophagocyticSequencePAED ETOP150/DEXA10, HLH, C1 (PID665) -|- C2 (PID666) -|- C3+ (PID667)ChemotherapyChemo-substanceDexamethasoneEtoposideChemo-substanceDexamethasoneEtoposideChemo-substanceDexamethasoneEtoposideChemo-substanceDexamethasoneEtoposideNo. Substances2 RadiotherapySupportive therapySupportive substanceBalanced Crystalloid SolutionCiclosporin ACotrimoxazoleFluconazoleGranisetronSupportive substanceBalanced Crystalloid SolutionCiclosporin ACotrimoxazoleFluconazoleGranisetronSupportive substanceBalanced Crystalloid SolutionCiclosporin ACotrimoxazoleFluconazoleGranisetronSupportive substanceBalanced Crystalloid SolutionCiclosporin ACotrimoxazoleFluconazoleGranisetronNo. Substances345Protocol classificationTherapy classificationcurrent standardIntensityStandard doseTherapy indicationFirst lineTherapy phaseInductionMaintenanceTherapy intentioncurativeRisksEmetogenicityEmetogenicity (MASCC/ESMO) only studiesPublicationAuthorEhl SDiseaseHämophagozytische LymphohistiozytoseOriginCenter for Chronic Immunodeficiency, Faculty of Medicine, University of Freiburg, Freiburg, Germany, HLH-94Protocols in Revision 3 protocols foundProtocols under revision.PAED Etoposide 150 / Dexamethasone (5 / 2.5 / 1.25), Hemophagocytic Lymphohistiocytosis, cycle 2 (PID666)PAED Etoposide 150 / Dexamethasone 10, Hemophagocytic Lymphohistiocytosis, Cycle 1 (PID665)PAED Etoposide 150 / Dexamethasone 10, Hemophagocytic Lymphohistiocytosis, Cycle 3+ (PID667)